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Second Aid\biochemistry\metabolism

\Metabolism sites
\Enzyme terminology
\Rate-determining enzymes of metabolic processes
\Summary of pathways
\Glycolysis /ATP production
\Activated carriers
\Universal electron acceptors
\Hexokinase vs. glucokinase
\Glycolysis regulation, key enzymes
\Regulation by F2,6BP
\Pyruvate dehydrogenase complex
\Pyruvate dehydrogenase deficiency
\Pyruvate metabolism
\TCA cycle (Krebs cycle)
\Electron transport chain and oxidative phosphorylation
\Gluconeogenesis, irreversible enzymes
\HMP shunt (pentose phosphate pathway)
\Respiratory burst (oxidative burst)
\Glucose-6-phosphate dehydrogenase deficiency
\Disorders of fructose metabolism
\Disorders of galactose metabolism
\Sorbitol
\Lactase deficiency
\Amino acids
\Urea cycle
\Transport of ammonium by alanine and glutamate
\Hyperammonemia
\Ornithine transcarbamoylase (OTC) deficiency
\Amino acid derivatives
\Catecholamine synthesis
\Phenylketonuria
\Alkaptonuria (ochronosis)
\Albinism
\Homocystinuria
\Cystinuria
\Maple syrup urine disease
\Hartnup disease
\Glycogen regulation by insulin and glucagon/epinephrine
\Glycogen
\Glycogenolysis/glycogen synthesis
\Glycogen storage diseases
\Lysosomal storage diseases
\Lysosomal storage diseases (continued)
\Fatty acid metabolism
\Ketone bodies
\Metabolic fuel use
\Metabolic fuel use (continued)
\Cholesterol synthesis
\Lipid transport, key enzymes
\Major apolipoproteins
\Lipoprotein functions
\Familial dyslipidemias
\Abeta-lipoproteinemia

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